ABSTRACT
Double Outlet Right Ventricle (DORV) is associated to a wide set of cardiovascular anomalies. We report a rare
combination of congenital cardiac malformation of DORV with unrestrictive non-committed interventricular
communication, persistent left superior vena cava, sub pulmonary stenosis and aberrant right Subclavian artery.
Read complete pubblications here
ABSTRACT
We show a brief report of two common arterial trunk cases (CAT) with different arrhythmias and discuss anatomy,
clinical and diagnostic management. The burden of volume and pressure overload of this cardiac malformation
may predispose to different types of arrhythmia before and after surgical repair. Because of labile
hemodynamic state in this group of patients, prompt diagnosis of any arrhythmia is mandatory as the devastating
factor on prognosis. The first patient with a diagnosis of CAT Type II Collett and Edwards (CE) had a particular
history with HIV seropositive mother assuming antiretroviral therapy during pregnancy, who presented hyperbilirubinemia
and liver dysfunction at birth, and re-entry atrial tachycardia after repair. The second patient
had CAT Type I CE with a partial anomalous venous connection of left superior pulmonary vein and uncommon
type of atrial tachycardia with dual AV nodal physiology.
Read complete pubblications here
ABSTRACT
Fetal arrhythmias reach up around 10% of the total third-level perinatal cardiology references. Sustained bradycardia
is defined as a baseline fetal heart rate (FHR) of less than 110 bpm sustained for at least 10 min. The overall
incidence of malignant fetal bradyarrhythmias, such as complete atrioventricular block (AVB) and channellopathies,
is relatively rare, 1:5000 pregnancies, but represents a serious emergency for the gynecologist, neonatologists,
and pediatric cardiologists. Fetal complete AVB is strongly associated with maternal connective tissue
disease, but it can be also associated with congenital heart disease and usually with a poorer prognosis with high
risk of fetal hydrops and abortion. Currently, the treatment of severe fetal bradyarrhythmias is principally pharmacological
and aims to increase the FHR, besides an early resolution of underlying causes, when possible, and a
promptly management of fetal heart failure. Intrauterine electrostimulation nowadays is an experimental pioneering
method, reserved for limited selected cases.
Read complete pubblications here
